incontinentia pigmenti achromians, a congenital neurocutaneous syndrome, not present at birth but appearing in early life, characterized by the presence of peculiar whorled, linear, and splatter-like patterns of hypopigmentation and often associated with other abnormalities, including hair loss and ocular, musculoskeletal, and mental disturbances. Also called hypomelanosis of Ito. Should not be confused with incontinentia pigmenti.
