choroideremia /kôr′oidərē′mē·ə/ [Gk, chorion, skin + eidos, form + erēmia, destitution] , hereditary primary degeneration of the retina, transmitted as an X-linked trait and beginning in the first decade of life. In males, the earliest symptom is usually night blindness, followed by constricted visual field and eventual blindness as the degeneration of the pigment epithelium of the retina progresses to complete atrophy. In females, it is nonprogressive; usually there is normal vision and often an atypical pigmentary retinopathy.
