Hallervorden-Spatz syndrome

Hallervorden-Spatz syndrome /hol″ərfôr′dən shpots/ [Julius Hallervorden, German neurologist, 1882–1965; H. Spatz, German neurologist, 1888–1969] , a progressive degenerative neurological disease of children, with symptoms of parkinsonism. It is characterized by rigidity, athetosis, and dementia. The cause is an accumulation of iron pigments in the globus pallidus and substantia nigra. Treatment is similar to that of Parkinson’s disease and Huntington’s chorea.

Child with Hallervorden-Spatz syndrome: abnormal posturing (Newton, 1995)